Pleuropulmonary blastoma

Pleuropulmonary blastoma (PPB) is a rare cancer originating in the lung or pleural cavity. It occurs most often in infants and young children^[1] but also has been reported in adults.^[2] In a retrospective review of 204 children with lung tumors, pleuropulmonary blastoma and carcinoid tumor were the most common primary tumors (83% of the 204 children had secondary tumors spread from cancers elsewhere in the body).^[1] Pleuropulmonary blastoma is regarded as malignant. The male:female ratio is approximately one.